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Piotrowski Z , Canter DJ , Kutikov A , Al-Saleem T , Pei J , Testa JR , Uzzo RG
Metanephric adenofibroma: robotic partial nephrectomy of a large Wilms' tumor variant
Canadian Journal of Urology. 2010 Aug;17(4) :5309-5312
PMID: ISI:000281313900013   
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Abstract
Purpose: A case of the rare, benign, Wilms' tumor (WT) variant, metanephric adenofibroma (MAF), is presented. Materials and methods: The patient is a 21-year-old female with an incidentally discovered enhancing renal mass. The diagnosis, workup and treatment are outlined. Results: The 19 cm renal mass was ultimately resected via robot-assisted partial nephrectomy. Pathologic diagnosis at our institution was confirmed as a MAF by the National Wilms' Tumor Study Group (NWTSG). Conclusion: Difficult to differentiate from WT, it is imperative that MAF be recognized and appropriately diagnosed because unlike adult WT, the natural history of MAF is indolent and adjuvant chemo/radiation therapy is rarely necessary. This case reinforces the importance of review of potential WT variants by the NWTSG.
Notes
Piotrowski, Zachary Canter, Daniel J. Kutikov, Alexander Al-Saleem, Tahseen Pei, Jianming Testa, Joseph R. Uzzo, Robert G. Fox Chase Cancer Center via Kidney Cancer Keystone Program Funds for this publication were provided by Fox Chase Cancer Center via institutional support of the Kidney Cancer Keystone Program. 10 Canadian j urology; 2330 ward st, ste 604, st laurent, quebec h4m 2v6, canada 643qq